Anaesthetic Management In A Pediatric Patient With Malignant Transformation Of Hepatic Adenoma In Glycogen Storage Disease Type 1 (Von-Gierke) For Liver Transplantation: A Case Report

Glycogen storage disease type Ia (GSD-Ia; Von Gierke disease) is an inherited disease caused by glucose-6-phosphatase deficiency. Perioperative management of patients with GSD has important implications for anaesthesiologists due to different system involvements. Continue reading →